Neuron
Volume 92, Issue 2, 19 October 2016, Pages 383-391
ReportPoly(GR) in C9ORF72-Related ALS/FTD Compromises Mitochondrial Function and Increases Oxidative Stress and DNA Damage in iPSC-Derived Motor Neurons
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Keywords
ALS
C9ORF72
DNA damage
DPR
FTD
iPSC
mitochondria
oxidative stress
RAN translation
repeats
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